00596nz a2200217n 4500 230628|||anznnbab||||||||||||||a|||||||d homoit0002818 https://homosaurus.org/v3/homoit0002818 homoit 17-beta hydroxysteroid dehydrogenase 3 deficiency 17-beta Intersex variations https://homosaurus.org/v3/homoit0000669 People with 17-beta hydroxysteroid dehydrogenase 3 deficiency, abbreviated as "17-beta," have XY chromosomes and testes, but their bodies do not have one of the enzymes needed to synthesize testosterone. Most people with 17-beta are born with a vulva and vagina, and their testes are most often undescended. Some people with 17-beta will be born with genitals that do not clearly resemble a typical penis or a typical vulva. Some will have a penis that may be smaller than typical (known as a micropenis), and the urethra may open on the underside of the penis rather than at the tip (known as hypospadias). In adolescence, people with 17-beta will often develop some secondary sex characteristics associated with a typical testosterone puberty.